Primary intracranial malignant peripheral nerve sheath tumour responding to chemotherapy

• Autores: Francisco Zambrana, David Vicente Baz
• Localización: Clinical & translational oncology, ISSN 1699-048X, Vol. 12, Nº. 3, 2010, págs. 231-233
• Idioma: inglés
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• Resumen

  • Malignant peripheral nerve sheath tumours (MPNST) are a rare variety of soft tissue sarcomas (STS) arising from major peripheral nerve branches and typically located in the lower extremity, chest wall or the retroperitoneum.

    It is a biologically aggressive neoplasm for which the treatment of choice is surgery, but usually requires a multimodality approach, having been generally labelled as chemoresistant. We present a case of MPNST located intracranially with a good response to chemotherapy.