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Granulomatous Vasculitis

  • Autores: Aman Sharma, Sunil Dogra, Kusum Sharma
  • Localización: Dermatologic clinics, ISSN 0733-8635, Vol. 33, Nº. 3, 2015 (Ejemplar dedicado a: Granulomatous Disorders of Adult Skin), págs. 475-487
  • Idioma: inglés
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  • Resumen
    • Vasculitides are uncommon disorders, characterized by inflammation of the blood vessels resulting either in ischemia or hemorrhage. They are commonly classified as small-, medium-, or large-vessel vasculitides. Antineutrophil cytoplasmic antibody-associated vasculitis is an important group of small-vessel vasculitis. This group includes granulomatous vasculitides, namely, granulomatosis with polyangiitis (GPA), eosinophilic granulomatosis with polyangiitis (EGPA), and nongranulomatous vasculitis, namely, microscopic polyangiitis (MPA). Classic polyarteritis nodosa (PAN) is a granulomatous medium-vessel vasculitis. This review discusses the classification, etiopathogenesis, clinical features, and management of GPA, MPA, EGPA and PAN.


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