Granulomatous Lymphoproliferative Disorders: Granulomatous Slack Skin and Lymphomatoid Granulomatosis

• Autores: Pamela Gangar, Sangeetha Venkatarajan
• Localización: Dermatologic clinics, ISSN 0733-8635, Vol. 33, Nº. 3, 2015 (Ejemplar dedicado a: Granulomatous Disorders of Adult Skin), págs. 489-496
• Idioma: inglés
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• Resumen

  • Granulomatous cutaneous T-cell lymphomas (CTCL) and lymphomatoid granulomatosis are considered granulomatous lymphoproliferative disorders. The most common types of granulomatous CTCL are granulomatous mycosis fungoides and granulomatous slack skin. Lymphomatoid granulomatosis is a rare Epstein-Barr virus driven lymphoproliferative disorder. This article reviews the etiopathogenesis, clinical presentation, systemic associations, and management of both granulomatous slack skin syndrome and lymphomatoid granulomatosis.