Fibrosarcoma de arteria pulmonar simulando un síndrome de Hughes Stovin

• Daniel Erlij ^[1] ; Susana Michalland ^[1] ; Óscar Neira ^[1] ; Cristina Fernández ^[2] ; Verónica Wolff ^[1]
  1. [1] Universidad de Chile

     Universidad de Chile

     Santiago, Chile

     
  2. [2] Instituto Nacional del Tórax Departamento de Anatomía Patológica
• Localización: Revista Médica de Chile, ISSN-e 0034-9887, Vol. 142, Nº. 11, 2014
• Idioma: español
• Títulos paralelos:
  • Pulmonary artery sarcoma mimicking a Hughes Stovin syndrome. Report of one case
• Enlaces
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• Resumen

  • Pulmonary artery sarcoma is an uncommon entity with high mortality. Its clinical presentation is usually indistinguishable from pulmonary embolism, which leads to a significant delay in diagnosis. Hughes-Stovin syndrome is characterized by venous thrombosis and aneurysms of the pulmonary or bronchial artery. We report a 59 year-old female with a history of recurrent pulmonary embolism. In the last thromboembolic episode a pulmonary artery aneurysm was found on a CT scan. The patient was operated performing a left inferior lobectomy. The patient died five days after surgery and the pathological examination of the surgical piece revealed a pulmonary artery sarcoma.